Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale

Title

Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale

Creator

Subramony S H; May W; Lynch D; Gomez C; Fischbeck K; Hallett M; Taylor P; Wilson R; Ashizawa T; Cooperative Ataxia Group

Publisher

Neurology

Date

2005

Subject

Adolescent; Adult; Age of Onset; Arm/pp [Physiopathology]; Brain Stem/pp [Physiopathology]; Disease Progression; Female; Friedreich Ataxia/di [Diagnosis]; Friedreich Ataxia/pp [Physiopathology]; Gait Disorders; Neurologic/di [Diagnosis]; Gait Disorders; Neurologic/et [Etiology]; Gait Disorders; tone and motor problems; Friedreich's ataxia; tool development; scale development; Friedrich's Ataxia Scale

Description

Measuring the severity of neurologic dysfunction in patients with inherited ataxias, including Friedreich ataxia (FA), is difficult because of the variable rate of progression, the variable age at onset and the variety of neural systems that may be affected. The authors discuss the problems related to rating scales in the ataxias, report a neurologic rating scale for FA, and demonstrate acceptable interrater reliability of the instrument.

Rights

Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).

Citation

Subramony S H; May W; Lynch D; Gomez C; Fischbeck K; Hallett M; Taylor P; Wilson R; Ashizawa T; Cooperative Ataxia Group, “Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale,” Pediatric Palliative Care Library, accessed September 16, 2021, https://pedpalascnetlibrary.omeka.net/items/show/16820.

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