Spinal muscular atrophy type 1: is long-term mechanical ventilation ethical?

Title

Spinal muscular atrophy type 1: is long-term mechanical ventilation ethical?

Creator

Ryan MM; Kilham H; Jacobe S; Tobin B; Isaacs D

Publisher

Journal Of Paediatrics And Child Health

Date

2007

Subject

Humans; Intensive Care Units; New South Wales; Respiration; Spinal Muscular Atrophies of Childhood; quality of life; Pediatric; ICU Decision Making; Artificial/ethics

Description

We present a baby with spinal muscular atrophy type 1, an inherited disorder causing progressive weakness, leading to complete paralysis of respiratory, facial and limb muscles. Without intervention, death occurs in infancy due to respiratory failure. Mechanical ventilatory support can prolong life, but the child's quality of life is highly debatable. We discuss the appropriateness of initiating and continuing intensive care for this child and others in a similar position.
2007

Rights

Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).

Type

Journal Article

Citation List Month

Backlog

Pages

237-242

Issue

4

Volume

43

Citation

Ryan MM; Kilham H; Jacobe S; Tobin B; Isaacs D, “Spinal muscular atrophy type 1: is long-term mechanical ventilation ethical?,” Pediatric Palliative Care Library, accessed September 26, 2021, https://pedpalascnetlibrary.omeka.net/items/show/14162.

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