Sleep problems in children with Sanfilippo syndrome.

Title

Sleep problems in children with Sanfilippo syndrome.

Creator

Colville GA; Watters JP; Yule W; Bax M

Publisher

Developmental Medicine And Child Neurology

Date

1996

Subject

Child; Female; Humans; Male; Questionnaires; Longitudinal Studies; Time Factors; Preschool; Sleep Disorders/etiology; Sleep Disorders/therapy; Mucopolysaccharidosis III/classification; Mucopolysaccharidosis III/complications

Description

Sanfilippo syndrome is a rare degenerative disorder which has severe intellectual and behavioural sequelae, commonly including sleep problems. A parental questionnaire was used to gather information on the sleep patterns of 80 children with Sanfilippo syndrome (mean age 10 years 2 months). The majority were found to have sleep problems (78%). Many also exhibited other distressing and unusual night time behaviours (staying up all night, chewing the bedclothes or crying out suddenly), and a few laughed or sang. Such problems may have been more severe in those with Sanfilippo syndrome type B. In four of the families offered individually tailored behaviour-management advice there was immediate improvement, which was maintained at followup in two cases. These results demonstrate the usefulness of even such a minimal intervention, even in a very difficult population such as this.
1996

Rights

Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).

Type

Journal Article

Citation List Month

Backlog

Pages

538-44

Issue

6

Volume

38

Citation

Colville GA; Watters JP; Yule W; Bax M, “Sleep problems in children with Sanfilippo syndrome.,” Pediatric Palliative Care Library, accessed September 20, 2021, https://pedpalascnetlibrary.omeka.net/items/show/11938.

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