Problem behaviors associated with deletion Prader-Willi, Smith-Magenis, and cri du chat syndromes

Title

Problem behaviors associated with deletion Prader-Willi, Smith-Magenis, and cri du chat syndromes

Creator

Clarke D J; Boer H

Publisher

American Journal of Mental Retardation

Date

1998

Subject

behavioral problems; Cri-du-chat; trajectory; characteristics

Description

Problem behaviors of individuals who had one of three chromosome deletion disorders (5p- cri-du-chat, 15q- Prader-Willi, or 17p- Smith-Magenis) were investigated. The Aberrant Behavior Checklist was used. Results were contrasted with those of two groups of people with mental retardation who were described in other studies. The checklist rates many, but not all, potentially relevant behaviors. Eating abnormalities, known to be problematic in Prader-Willi syndrome, and sleep abnormalities, believed to be problematic in Smith-Magenis syndrome, were not included in the survey. All three disorders were associated with greater ratings of problem behaviors than the comparison groups on at least one subscale of the checklist. The results lend support to the partial specificity model of behaviors associated with genetically determined syndromes.

Rights

Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).

Citation

Clarke D J; Boer H, “Problem behaviors associated with deletion Prader-Willi, Smith-Magenis, and cri du chat syndromes,” Pediatric Palliative Care Library, accessed December 7, 2021, https://pedpalascnetlibrary.omeka.net/items/show/16614.

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