1
40
17
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1093/ptj/69.12.1099" target="_blank" rel="noreferrer noopener">http://doi.org/10.1093/ptj/69.12.1099</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Effect of hand splints on stereotypic hand behavior of girls with Rett syndrome: a replication study
Publisher
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Physical Therapy
Date
A point or period of time associated with an event in the lifecycle of the resource
1989
Subject
The topic of the resource
Humans; Female; Child Preschool; Reproducibility of Results; Splints; Stereotyped Behavior; Hand; Rett Syndrome/rehabilitation; tone and motor problems; Rett syndrome; physical intervention; hand splints; hand wringing
Creator
An entity primarily responsible for making the resource
Tuten H; Miedaner J
Description
An account of the resource
The purposes of this study were to replicate a recent report of the positive effects of hand splinting on the stereotypic hand movement of children with Rett syndrome and to evaluate the generality of these results to a different setting. Two 5-year-old girls diagnosed with early Stage-III Rett syndrome were introduced to hand splints in accordance with the multiple-baseline design used in the Naganuma and Billingsley study. Splint wear ranged from 30 to 50 days for the two subjects. Data were analyzed as a percentage of time and as actual time in minutes. Unlike the previous study, in which a decrease in hand-wringing behavior was noted, neither subject in our study demonstrated a decrease in stereotypic hand behavior or a subsequent increase in independent feeding skills when wearing the splints. There was also no evidence of increased hand wringing following withdrawal of the splints. The differences in ages of the subjects and different functional levels (stages) may have been contributing factors to the conflicting results and should be considered in managing this group of children.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1093/ptj/69.12.1099" target="_blank" rel="noreferrer noopener">10.1093/ptj/69.12.1099</a>
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Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
1989
Child Preschool
Female
Hand
hand splints
hand wringing
Humans
Miedaner J
physical intervention
Physical Therapy
Reproducibility of Results
Rett syndrome
Rett Syndrome/rehabilitation
splints
Stereotyped Behavior
tone and motor problems
Tuten H
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1054/ctim.2001.0436" target="_blank" rel="noreferrer noopener">http://doi.org/10.1054/ctim.2001.0436</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Effects of acupuncture on skin temperature in children with neurological disorders and cold feet: An exploratory study
Publisher
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Complementary Therapies in Medicine
Date
A point or period of time associated with an event in the lifecycle of the resource
2001
Subject
The topic of the resource
temperature regulation; Smith-Lemli-Opitz syndrome; progressive encephaolopathia; physical intervention; acupuncture
Creator
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Svedberg L E; Nordahl U E G; Lundeberg T C M
Description
An account of the resource
In a single subject design, acupuncture effects on peripheral skin temperature were studied in six children with cold feet associated with cerebral palsy, progressive encephalopathy or Smith-Lemli-Opitz syndrome. Skin temperature was measured at fixed points on the forehead, suprasternal fossa, hand dorsum and palm, foot dorsum and sole from a distance of 3 cm with a Raytek Raynger ST2L. Acupuncture needles were inserted in arms or legs with or without electrical stimulation. Three children displayed a brief rise in temperature in the hands and one in the feet. A tendency towards a cumulative effect in improved skin temperature occurred in two of three children receiving additional sessions. One child did not respond to acupuncture. It is possible that acupuncture may increase skin temperature in some children with cold extremities of neurological origin. Studies in larger groups are needed. © 2001 Harcourt Publishers Ltd.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1054/ctim.2001.0436" target="_blank" rel="noreferrer noopener">10.1054/ctim.2001.0436</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2001
Acupuncture
Complementary Therapies in Medicine
Lundeberg T C M
Nordahl U E G
physical intervention
progressive encephaolopathia
Smith-Lemli-Opitz syndrome
Svedberg L E
temperature regulation
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.rasd.2014.06.009" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.rasd.2014.06.009</a>
Dublin Core
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Title
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Comparing PECS and VOCA to promote communication opportunities and to reduce stereotyped behaviors by three girls with Rett syndrome
Publisher
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Research in Autism Spectrum Disorders
Date
A point or period of time associated with an event in the lifecycle of the resource
2014
Subject
The topic of the resource
Psychology; social; Rehabilitation; Quality of life; Education & Educational Research; Rett syndrome; autism; Psychiatry; spectrum disorders; developmental-disabilities; quality-of-life; disabilities; 2 boys; Augmentative and alternative communication; contact; Developmental; environmental stimuli; Indices of happiness; keyboard emulator; microswitch-based programs; motor disabilities; profound multiple disabilities; Stereotypies; tone and motor problems; physical intervention; Picture exchange communication systems; Vocal output communication aid
Creator
An entity primarily responsible for making the resource
Stasolla F; De Pace C; Damiani R; Di Leone A; Albano V; Perilli V
Description
An account of the resource
We compared PECS and VOCA intervention strategies to promote communication opportunities for three girls with Rett syndrome and severe to profound developmental disabilities. The first aim of the study was to assess the effectiveness of both aforementioned strategies by enhancing request and choices of preferred items by the participants involved to a caregiver. The second goal of the study was to assess the effects of the intervention program by reducing stereotyped behaviors (i.e. body rocking and hand movements). Finally, the third purpose was to carry out the indices of happiness and monitor quality of life concerning the participants exposed to the intervention program. The study was carried out according to an alternating treatments design with a final preference check phase for each participant. Results showed an increasing of independent requested and chosen items as well as of indices of happiness during intervention phases for all participants. Moreover, two of them chose VOCA strategy during preference checks phase, while the third one equally chose both strategies. Furthermore, a decreasing of stereotypies was observed during intervention phases for the three participants. Clinical, educational and psychological implications of the findings are discussed. (C) 2014 Elsevier Ltd. All rights reserved.
Identifier
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<a href="http://doi.org/10.1016/j.rasd.2014.06.009" target="_blank" rel="noreferrer noopener">10.1016/j.rasd.2014.06.009</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2 boys
2014
Albano V
Augmentative and alternative communication
Autism
contact
Damiani R
De Pace C
DEVELOPMENTAL
Developmental-disabilities
Di Leone A
Disabilities
Education & Educational Research
environmental stimuli
Indices of happiness
keyboard emulator
microswitch-based programs
motor disabilities
Perilli V
physical intervention
Picture exchange communication systems
profound multiple disabilities
Psychiatry
Psychology
Quality Of Life
quality-of-life
Rehabilitation
Research In Autism Spectrum Disorders
Rett syndrome
Social
spectrum disorders
Stasolla F
stereotypies
tone and motor problems
Vocal output communication aid
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.ridd.2014.09.017" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.ridd.2014.09.017</a>
Dublin Core
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Title
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Technological aids to support choice strategies by three girls with Rett syndrome
Publisher
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Research in Developmental Disabilities
Date
A point or period of time associated with an event in the lifecycle of the resource
2015
Subject
The topic of the resource
tone and motor problems; Rett syndrome; physical intervention; assistive technology; photocells; interface; personal computer; stereotyped movements
Creator
An entity primarily responsible for making the resource
Stasolla F; Perilli V; Di Leone A; Damiani R; Albano V; Stella A; Damato C
Description
An account of the resource
This study was aimed at extending the use of assistive technology (i.e., photocells, interface and personal computer) to support choice strategies by three girls with Rett syndrome and severe to profound developmental disabilities. A second purpose of the study was to reduce stereotypic behaviors exhibited by the participants involved (i.e., body rocking, hand washing and hand mouthing). Finally, a third goal of the study was to monitor the effects of such program on the participants' indices of happiness. The study was carried out according to a multiple probe design across responses for each participant. Results showed that the three girls increased the adaptive responses and decreased the stereotyped behaviors during intervention phases compared to baseline. Moreover, during intervention phases, the indices of happiness augmented for each girl as well. Clinical, psychological and rehabilitative implications of the findings are discussed.Copyright © 2014 Elsevier Ltd. All rights reserved.
Identifier
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<a href="http://doi.org/10.1016/j.ridd.2014.09.017" target="_blank" rel="noreferrer noopener">10.1016/j.ridd.2014.09.017</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2015
Albano V
Assistive technology
Damato C
Damiani R
Di Leone A
interface
Perilli V
personal computer
photocells
physical intervention
Research in Developmental Disabilities
Rett syndrome
Stasolla F
Stella A
stereotyped movements
tone and motor problems
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.rasd.2013.07.010" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.rasd.2013.07.010</a>
Dublin Core
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Title
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Promoting adaptive behaviors by two girls with Rett syndrome through a microswitch-based program
Publisher
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Research in Autism Spectrum Disorders
Date
A point or period of time associated with an event in the lifecycle of the resource
2013
Subject
The topic of the resource
Assistive technology; Indices of happiness; Locomotor behavior; Microswitches; Rett syndrome; adaptive behavior; adolescent; article; case report; child behavior; female; hand washing; happiness; human; locomotion; priority journal; school child; stereotypy; tone and motor problems; Rett syndrome; physical intervention; Wobble microswitch; optic sensors; stereotyped movements
Creator
An entity primarily responsible for making the resource
Stasolla F; Caffo A O
Description
An account of the resource
We assessed a microswitch-based program to improve self-determination to access to preferred stimuli and to foster locomotor behavior by two girls with Rett syndrome and multiple disabilities. To enhance the first behavior (access to preferred stimuli) a wobble microswitch (sensitive touch sensor) was used while for the second behavior (step responses) optic sensors were applied. A second aim of the study was to monitor indices of happiness as consequence of the use of assistive technology. Finally, a third objective of the study was the reduction of hand washing and body rocking related stereotypies. The study was carried out according to a multiple probe design across behaviors for both participants, where the two behaviors were first learned independently, then combined together. Results showed an increasing of performance and of indices of happiness and a decreasing of stereotyped behaviors for both participants during intervention phases. Practical, psychological and clinical implications of the findings are discussed. © 2013 Elsevier Ltd. All rights reserved.
Identifier
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<a href="http://doi.org/10.1016/j.rasd.2013.07.010" target="_blank" rel="noreferrer noopener">10.1016/j.rasd.2013.07.010</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2013
adaptive behavior
Adolescent
Article
Assistive technology
Caffo A O
Case Report
Child Behavior
Female
hand washing
Happiness
Human
Indices of happiness
locomotion
Locomotor behavior
Microswitches
optic sensors
physical intervention
Priority Journal
Research In Autism Spectrum Disorders
Rett syndrome
School Child
Stasolla F
stereotyped movements
stereotypy
tone and motor problems
Wobble microswitch
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.5014/ajot.46.2.134" target="_blank" rel="noreferrer noopener">http://doi.org/10.5014/ajot.46.2.134</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Comparative Effects of Bilateral Hand Splints and an Elbow Orthosis on Stereotypic Hand Movements and Toy Play In 2 Children with Rett Syndrome
Publisher
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American Journal of Occupational Therapy
Date
A point or period of time associated with an event in the lifecycle of the resource
1992
Subject
The topic of the resource
tone and motor problems; Rett syndrome; physical intervention; elbow orthosis; thumb abduction splints; stereotypic hand movements
Creator
An entity primarily responsible for making the resource
Sharpe PA
Description
An account of the resource
A single-subject rapidly alternating treatment design was used to compare the effectiveness of bilateral band splints and an elbow orthosis in decreasing stereotypic band behaviors and increasing toy play in 2 children with Rett syndrome. The subjects' responses were compared across three treatment conditions: no intervention, hand splints, and elbow orthosis. The order of the treatment phases was randomly selected for each subject. Data were collected in both a free-time condition and a toy-play condition; the outcome measures were stereotypic band movements and band-to-toy contact. Both subjects demonstrated a decrease in stereotypic band movements and a corresponding increase in toy contact with the use of the elbow orthosis. The bilateral hand splints bad no obvious treatment effect.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.5014/ajot.46.2.134" target="_blank" rel="noreferrer noopener">10.5014/ajot.46.2.134</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
1992
American Journal Of Occupational Therapy
elbow orthosis
physical intervention
Rett syndrome
Sharpe PA
stereotypic hand movements
Thumb abduction splints
tone and motor problems
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1177/0883073812438100" target="_blank" rel="noreferrer noopener">http://doi.org/10.1177/0883073812438100</a>
Dublin Core
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Title
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Botulinum Toxin Type A for the Treatment of Equinus Deformity in Patients With Mucopolysaccharidosis Type II
Publisher
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Journal of Child Neurology
Date
A point or period of time associated with an event in the lifecycle of the resource
2012
Subject
The topic of the resource
children; Pediatrics; Neurosciences & Neurology; management; botulinum toxin type A; cerebral-palsy; disease; equinus deformity; Hunter syndrome; hunter-syndrome; II; mucopolysaccharidosis type; recommendations; skeletal-muscle; tone and motor problems; MPSII; pharmacologic intervention; physical intervention; botulinum toxin type A; serial casting; physical therapy
Creator
An entity primarily responsible for making the resource
Nava E; Weber P; Gautschi M; Nuoffer J M; Grunt S
Description
An account of the resource
Mucopolysaccharidoses are lysosomal storage disorders that are caused by a deficiency in the enzymes that degrade glycosaminoglycans. The accumulation of glycosaminoglycans affects multiple systems, resulting in coarse facial features, short stature, organomegaly, and variable neurological changes from normal intelligence to severe mental retardation and spasticity. Effects on the musculoskeletal system include dysostosis multiplex, joint stiffness, and muscle shortening. This article reports 2 patients with mucopolysaccharidosis type II (Hunter syndrome) who showed progressive equinus deformity of the feet. Both patients were treated with intramuscular botulinum toxin type A injections in the gastrocnemius and the soleus muscles, followed by serial casting. In both patients, passive range of motion, muscle tone, and gait performance were significantly improved. Botulinum toxin type A injections followed by serial casting are a therapeutic option for contractures in patients with mucopolysaccharidosis. However, the long-term effects and the effect of application in other muscles remain unknown.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1177/0883073812438100" target="_blank" rel="noreferrer noopener">10.1177/0883073812438100</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2012
botulinum toxin type A
cerebral-palsy
Children
Disease
equinus deformity
Gautschi M
Grunt S
Hunter syndrome
hunter-syndrome
II
Journal of Child Neurology
Management
MPSII
mucopolysaccharidosis type
Nava E
Neurosciences & Neurology
Nuoffer J M
Pediatrics
pharmacologic intervention
physical intervention
Physical Therapy
Recommendations
serial casting
skeletal-muscle
tone and motor problems
Weber P
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1093/ptj/68.5.664" target="_blank" rel="noreferrer noopener">http://doi.org/10.1093/ptj/68.5.664</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Effect of hand splints on stereotypic hand behavior of three girls with Rett syndrome
Publisher
An entity responsible for making the resource available
Physical Therapy
Date
A point or period of time associated with an event in the lifecycle of the resource
1988
Subject
The topic of the resource
Child; Humans; Adolescent; Female; Syndrome; Splints; Stereotyped Behavior; Autistic Disorder; Hand; Intellectual Disability; Neuromuscular Diseases/rehabilitation; tone and motor problems; Rett syndrome; physical intervention; Thumb abduction splints; stereotypic hand behavior; finger-feeding skills; hand splints
Creator
An entity primarily responsible for making the resource
Naganuma G M; Billingsley F F
Description
An account of the resource
The purpose of this multiple baseline study was to examine the effect of bilateral hand splints on the persistent stereotypic hand movements of three adolescent girls with Rett syndrome. Among the most characteristic features of Rett syndrome are stereotypic hand-writing and hand-biting behavior and loss of previously acquired functional hand skills. The hand splints used in this study consisted of cuffs encircling the palm that positioned the subjects' thumbs in abduction. Duration percentages of subjects' stereotypic hand behavior and functional hand use were calculated from five-minute videotaped segments recorded during a finger-feeding condition and a free-time condition. All three subjects demonstrated a decrease in the amount of time spent in stereotypic hand behavior after application of hand splints, and one subject showed an increase in finger-feeding skills while wearing hand splints. Limitations of the study are discussed, and suggestions for clinical application and future research are offered.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1093/ptj/68.5.664" target="_blank" rel="noreferrer noopener">10.1093/ptj/68.5.664</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
1988
Adolescent
Autistic disorder
Billingsley F F
Child
Female
finger-feeding skills
Hand
hand splints
Humans
Intellectual Disability
Naganuma G M
Neuromuscular Diseases/rehabilitation
physical intervention
Physical Therapy
Rett syndrome
splints
Stereotyped Behavior
stereotypic hand behavior
Syndrome
Thumb abduction splints
tone and motor problems
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.braindev.2008.03.007" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.braindev.2008.03.007</a>
Dublin Core
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Title
A name given to the resource
Sleep disordered breathing in childhood-onset acid maltase deficiency
Publisher
An entity responsible for making the resource available
Brain and Development
Date
A point or period of time associated with an event in the lifecycle of the resource
2009
Subject
The topic of the resource
Male; Child; Humans; Adolescent; Female; Retrospective Studies; Polysomnography; Positive-Pressure Respiration; Respiratory Function Tests; Muscle Weakness; Blood Gas Analysis; Quality of Life; Respiration; Glycogen Storage Disease Type II/pp [Physiopathology]; Sleep Apnea Syndromes/pp [Physiopathology]; Sleep Apnea Syndromes/th [Therapy]; Muscle Strength; Respiration Disorders/pp [Physiopathology]; Respiration Disorders/th [Therapy]; Sleep/ph [Physiology]; breathing difficulties; glycogen storage disease type II; physical intervention; non-invasive positive pressure ventilation; sleep apnea
Creator
An entity primarily responsible for making the resource
Nabatame S; Taniike M; Sakai N; Kato-Nishimura K; Mohri I; Kagitani-Shimono K; Okinaga T; Tachibana N; Ozono K
Description
An account of the resource
OBJECTIVES: To clarify the feature of sleep disordered breathing (SDB) associated with childhood-onset acid maltase deficiency (AMD): the progressive nature of SDB and the stage of AMD.;STUDY DESIGN: We retrospectively studied 4 patients with childhood-onset AMD by analyzing the results of neurological examinations for muscle wasting and muscle strength and the data on venous gas and from a pulmonary function test and nocturnal polysomnography (PSG).;RESULTS: Three out of the 4 patients showed muscular symptoms including myalgia, lordoscoliosis, muscle wasting and muscle weakness. They also complained of sleep-related symptoms such as tiredness in the morning and daytime sleepiness. All of them showed SDB by PSG, even in a patient in the earliest stage who exhibited no signs or symptoms of muscle weakness. In 3 patients, noninvasive intermittent positive pressure ventilation during sleep was introduced; and thereafter sleep-related symptoms were resolved and no lower respiratory infection reoccurred. Although their quality of life was improved, no improvement of respiratory function was shown by spirometry over a 2-year follow-up period.;CONCLUSIONS: SDB seems to be common in childhood-onset AMD, which is not always accompanied by daytime muscular symptoms, especially in mild patients. PSG should be utilized for detecting SDB, which could be one of the earliest signs of respiratory muscle involvement in childhood-onset AMD.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1016/j.braindev.2008.03.007" target="_blank" rel="noreferrer noopener">10.1016/j.braindev.2008.03.007</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2009
Adolescent
Blood Gas Analysis
Brain and Development
breathing difficulties
Child
Female
glycogen storage disease type II
Glycogen Storage Disease Type II/pp [Physiopathology]
Humans
Kagitani-Shimono K
Kato-Nishimura K
Male
Mohri I
Muscle Strength
Muscle Weakness
Nabatame S
non-invasive positive pressure ventilation
Okinaga T
Ozono K
physical intervention
Polysomnography
Positive-Pressure Respiration
Quality Of Life
Respiration
Respiration Disorders/pp [Physiopathology]
Respiration Disorders/th [Therapy]
Respiratory Function Tests
Retrospective Studies
Sakai N
Sleep apnea
Sleep Apnea Syndromes/pp [Physiopathology]
Sleep Apnea Syndromes/th [Therapy]
Sleep/ph [Physiology]
Tachibana N
Taniike M
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1620/tjem.214.327" target="_blank" rel="noreferrer noopener">http://doi.org/10.1620/tjem.214.327</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Olfactory stimulation using black pepper oil facilitates oral feeding in pediatric patients receiving long-term enteral nutrition
Publisher
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Tohoku Journal of Experimental Medicine
Date
A point or period of time associated with an event in the lifecycle of the resource
2008
Subject
The topic of the resource
feeding difficulties; Costello syndrome; lissencephaly type I; physical intervention; black pepper oil; increased oral intake; enteral nutrition
Creator
An entity primarily responsible for making the resource
Munakata M; Kobayashi K; Niisato-Nezu J; Tanaka S; Kakisaka Y; Ebihara T; Ebihara S; Haginoya K; Tsuchiya S T; Onuma A
Description
An account of the resource
Patients with severe neurological disorders often require enteral nutrition (EN). Since long-term EN can cause multiple complications, reinstating the oral intake of food is beneficial. Olfactory stimulation using black pepper oil (BPO), a strong appetite stimulant, was reported to facilitate swallowing in order people. Therefore, the effects of olfactory stimulation with BPO were investigated in pediatric patients receiving long-term EN due to neurological disorders. The effects of scenting with BPO for 1 min immediately before every meal were evaluated in ten patients: 4 boys and 6 girls, aged 19-97 months (51 +/- 26 months). The neurological disorders included periventricular leukomalacia (3 patients), hypoxic ischemic encephalopathy (3). Costello syndrome (1), Russell-Silver syndrome (1), Miller-Dieker syndrome (1), and cerebral palsy of unknown etiology (1). In eight of these patients, BPO intervention was continued for 3 months. Five of these eight patients showed increases in the amount of oral intake with desirable effects including facilitated swallowing movement, although complete elimination of the need for EN was not achieved. In the other three patients: BPO intervention was not effective; severe cerebral tissue loss, profound malformation or intractable seizures seemed to reduce the efficacy of BPO. In two cases, BPO intervention was discontinued due to cough or because the odor of BPO was unbearable to the family. In conclusion, olfactory stimulation with BPO facilitated oral intake in a subset of patients on long-term EN. BPO stimulation may be useful or facilitating oral intake when used in combination with conventional methods. © 2008 Tohoku University Medical Press.
Identifier
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<a href="http://doi.org/10.1620/tjem.214.327" target="_blank" rel="noreferrer noopener">10.1620/tjem.214.327</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2008
black pepper oil
costello syndrome
Ebihara S
Ebihara T
Enteral Nutrition
feeding difficulties
Haginoya K
increased oral intake
Kakisaka Y
Kobayashi K
lissencephaly type I
Munakata M
Niisato-Nezu J
Onuma A
physical intervention
Tanaka S
Tohoku Journal of Experimental Medicine
Tsuchiya S T
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1017/s0012162200000463" target="_blank" rel="noreferrer noopener">http://doi.org/10.1017/s0012162200000463</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Air swallowing in Rett syndrome
Publisher
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Developmental Medicine and Child Neurology
Date
A point or period of time associated with an event in the lifecycle of the resource
2000
Subject
The topic of the resource
Child; Humans; Adult; Adolescent; Female; Child Preschool; Risk Factors; Video Recording; Fluoroscopy; Aerophagy/di [Diagnosis]; Rett Syndrome/di [Diagnosis]; Aerophagy/pp [Physiopathology]; Aerophagy/px [Psychology]; Apnea/di [Diagnosis]; Apnea/pp [Physiopathology]; Apnea/px [Psychology]; Feeding Behavior/ph [Physiology]; Larynx/pp [Physiopathology]; Rett Syndrome/pp [Physiopathology]; Rett Syndrome/px [Psychology]; Stress Psychological/co [Complications]; feeding difficulties; Rett syndrome; physical intervention; hollow tube; gum shield; palatal training devices; air bloat; hyperventilation
Creator
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Morton R E; Pinnington L; Ellis R E
Description
An account of the resource
The possible causes of excessive swallowing of air leading to bloating, which is common in Rett syndrome (RS), were investigated during feeding and at rest. Seven individuals with RS aged between 4 and 33 years (three with air bloat) underwent feeding videoflouroscopy and concurrent respiration monitoring. The results were compared with a randomly selected group of 11 individuals, aged between 2 and 16 years, with quadriplegic cerebral palsy and feeding problems, some of whom had mild air bloat. All individuals from both groups had isolated pharyngeal swallows and several mouth breathed; this may account for some air swallowing but not the severe air bloat characteristic of RS. Thirty-three individuals with RS aged between 3 and 44 years were monitored for nasal respiration, chest movements, swallowing, and vocal cord position at rest (between feeding). Twenty had air bloat, 17 of whom swallowed air during breath-holding in the same way, and three gulped air during hyperventilation. Of the 13 without air bloat, eight did not have recurrent breath-holding and five did, but without concurrent air swallowing. Several methods for reducing air swallowing in apnoea were investigated. The most successful was a dummy with an air leak, but this was poorly tolerated and could only be used for short periods of time. Apnoeas and air bloat are often worse when individuals are distressed and may in some individuals be reduced by anxiolytic medications.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1017/s0012162200000463" target="_blank" rel="noreferrer noopener">10.1017/s0012162200000463</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2000
Adolescent
Adult
Aerophagy/di [Diagnosis]
Aerophagy/pp [Physiopathology]
Aerophagy/px [Psychology]
air bloat
Apnea/di [Diagnosis]
Apnea/pp [Physiopathology]
Apnea/px [Psychology]
Child
Child Preschool
Developmental Medicine and Child Neurology
Ellis R E
Feeding Behavior/ph [Physiology]
feeding difficulties
Female
Fluoroscopy
gum shield
hollow tube
Humans
hyperventilation
Larynx/pp [Physiopathology]
Morton R E
palatal training devices
physical intervention
Pinnington L
Rett syndrome
Rett Syndrome/di [Diagnosis]
Rett Syndrome/pp [Physiopathology]
Rett Syndrome/px [Psychology]
Risk Factors
Stress Psychological/co [Complications]
Video Recording
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1002/14651858.CD009456.pub2" target="_blank" rel="noreferrer noopener">http://doi.org/10.1002/14651858.CD009456.pub2</a>
Dublin Core
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Title
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Interventions for oropharyngeal dysphagia in children with neurological impairment
Publisher
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The Cochrane Database of Systematic Reviews
Date
A point or period of time associated with an event in the lifecycle of the resource
2012
Subject
The topic of the resource
neurological impairment; Rett syndrome; Down syndrome; cerebral palsy; traumatic brain injury; stroke; myotonic dystrophy; oropharyngeal dysphagia; feeding difficulties; oral sensorimotor intervention; physical intervention; sensorimotor intervention; lip strengthening intervention
Creator
An entity primarily responsible for making the resource
Morgan A T; Dodrill P; Ward E C
Description
An account of the resource
BACKGROUND: Oropharyngeal dysphagia encompasses problems with the oral preparatory phase of swallowing (chewing and preparing the food), oral phase (moving the food or fluid posteriorly through the oral cavity with the tongue into the back of the throat) and pharyngeal phase (swallowing the food or fluid and moving it through the pharynx to the oesophagus). Populations of children with neurological impairment who commonly experience dysphagia include, but are not limited to, those with acquired brain impairment (for example, cerebral palsy, traumatic brain injury, stroke), genetic syndromes (for example, Down syndrome, Rett syndrome) and degenerative conditions (for example, myotonic dystrophy). OBJECTIVES: To examine the effectiveness of interventions for oropharyngeal dysphagia in children with neurological impairment. SEARCH METHODS: We searched the following electronic databases in October 2011: CENTRAL 2011(3), MEDLINE (1948 to September Week 4 2011), EMBASE (1980 to 2011 Week 40)
, CINAHL (1937 to current)
, ERIC (1966 to current), PsycINFO (1806 to October Week 1 2011), Science Citation Index (1970 to 7 October 2011), Social Science Citation Index (1970 to 7 October 2011), Cochrane Database of Systematic Reviews, 2011(3), DARE 2011(3), Current Controlled Trials (ISRCTN Register) (15 October 2011), ClinicalTrials.gov (15 October 2011) and WHO ICTRP (15 October 2011). We searched for dissertations and theses using Networked Digital Library of Theses and Dissertations, Australasian Digital Theses Program and DART-Europe E-theses Portal (11 October 2011). Finally, additional references were also obtained from reference lists from articles. SELECTION CRITERIA: The review included randomised controlled trials and quasi-randomised controlled trials for children with oropharyngeal dysphagia and neurological impairment. DATA COLLECTION AND ANALYSIS: All three review authors (AM, PD and EW) independently screened titles and abstracts for inclusion and discussed results. In cases of uncertainty over whether an abstract met inclusion criterion, review authors obtained the full-text article and independently evaluated each paper for inclusion. The data were categorised for comparisons depending on the nature of the control group (for example, oral sensorimotor treatment versus no treatment). Effectiveness of the oropharyngeal dysphagia intervention was assessed by considering primary outcomes of physiological functions of the oropharyngeal mechanism for swallowing (for example, lip seal maintenance), the presence of chest infection and pneumonia, and diet consistency a child is able to consume. Secondary outcomes were changes in growth, child's level of participation in the mealtime routine and the level of parent or carer stress associated with feeding. MAIN RESULTS: Three studies met the inclusion criteria for the review. Two studies were based on oral sensorimotor interventions for participants with cerebral palsy compared to standard care and a third study trialled lip strengthening exercises for children with myotonic dystrophy type 1 compared to no treatment (Sjogreen 2010). A meta-analysis combining results across the three studies was not possible because one of the studies had participants with a different condition, and the remaining two, although using oral sensorimotor treatments, used vastly different approaches with different intensities and durations. The decision not to combine these was in line with our protocol. In this review, we present the results from individual studies for four outcomes: physiological functions of the oropharyngeal mechanism for swallowing, the presence of chest infection and pneumonia, diet consistency, and changes in growth. However, it is not possible to reach definitive conclusions on the effectiveness of particular interventions for oropharyngeal dysphagia based on these studies. One study had a high risk of attrition bias owing to missing data, had statistically significant differences (in weight) across experimental and control groups at baseline, and did not describe other aspects of the trial sufficiently to enable assessment of other potential risks of bias. Another study was at high risk of detection bias as some outcomes were assessed by parents who knew whether their child was in the intervention or control group. The third study overall seemed to be at low risk of bias, but like the other two studies, suffered from a small sample size. AUTHORS' CONCLUSIONS: The review demonstrates that there is currently insufficient high-quality evidence from randomised controlled trials or quasi-randomised controlled trials to provide conclusive results about the effectiveness of any particular type of oral-motor therapy for children with neurological impairment. There is an urgent need for larger-scale (appropriately statistically powered), randomised trials to evaluate the efficacy of interventions for oropharyngeal dysphagia.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1002/14651858.CD009456.pub2" target="_blank" rel="noreferrer noopener">10.1002/14651858.CD009456.pub2</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2012
Cerebral Palsy
Dodrill P
Down Syndrome
feeding difficulties
lip strengthening intervention
Morgan A T
myotonic dystrophy
neurological impairment
oral sensorimotor intervention
oropharyngeal dysphagia
physical intervention
Rett syndrome
sensorimotor intervention
Stroke
The Cochrane Database of Systematic Reviews
traumatic brain injury
Ward E C
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.nmd.2004.09.004" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.nmd.2004.09.004</a>
Dublin Core
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Title
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Sleep disordered breathing in spinal muscular atrophy
Publisher
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Neuromuscular Disorders
Date
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2004
Subject
The topic of the resource
Child; Cyclic AMP; Response Element-Binding Protein; Disease Progression; Female; Humans; Male; Muscle; Skeletal/pa [Pathology] Muscle; breathing difficulties; SMA1; physical intervention; non-invasive positive pressure ventilation; disordered breathing
Creator
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Mellies U; Dohna-Schwake C; Stehling F V T
Description
An account of the resource
Sleep disordered breathing is a common but under-diagnosed complication causing sleep disturbance and daytime symptoms in children with spinal muscular atrophy. Non-invasive (positive pressure) ventilation is an established treatment of respiratory failure; its role in treatment of sleep disordered breathing though remains controversial. Aim of this study was to verify the hypothesis that nocturnal non-invasive ventilation has beneficial impact on breathing during sleep, sleep quality and daytime complaints in children with spinal muscular atrophy. Twelve children with spinal muscular atrophy type I or II (7.8+/-1.9 years) underwent polysomnography and were asked to fill out a symptom questionnaire. Seven patients (six with spinal muscular atrophy I and one with spinal muscular atrophy II) had sleep disordered breathing and received non-invasive ventilation during sleep. Five less severely affected patients (one with spinal muscular atrophy I and four with spinal muscular atrophy II) had no sleep disordered breathing and served as reference group. Patients were restudied after 6-12 months. In patients with sleep disordered breathing both sleep architecture and disease related symptoms were significantly worse than in the reference-group. Non-invasive ventilation during sleep completely eliminated disordered breathing, normalized sleep architecture and improved symptoms (P<0.05 for all). In children with spinal muscular atrophy sleep disordered breathing may cause relevant impairment of sleep and well-being. Both can be highly improved by nocturnal non-invasive ventilation.
Identifier
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<a href="http://doi.org/10.1016/j.nmd.2004.09.004" target="_blank" rel="noreferrer noopener">10.1016/j.nmd.2004.09.004</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2004
breathing difficulties
Child
Cyclic AMP
Disease Progression
disordered breathing
Dohna-Schwake C
Female
Humans
Male
Mellies U
Muscle
Neuromuscular Disorders
non-invasive positive pressure ventilation
physical intervention
Response Element-Binding Protein
Skeletal/pa [Pathology] Muscle
SMA1
Stehling F V T
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.3109/17518423.2011.629374" target="_blank" rel="noreferrer noopener">http://doi.org/10.3109/17518423.2011.629374</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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The conductive environment enhances gross motor function of girls with Rett syndrome. A pilot study
Publisher
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Developmental Neurorehabilitation
Date
A point or period of time associated with an event in the lifecycle of the resource
2012
Subject
The topic of the resource
tone and motor problems; Rett syndrome; physical intervention; daily training program; treadmill
Creator
An entity primarily responsible for making the resource
Lotan M; Schenker R; Wine J; Downs J
Description
An account of the resource
INTRODUCTION: Rett syndrome (RTT) is a neurological disorder usually associated with a mutation in the MECP2 gene. Conductive Education (CE) is an educational approach that has not yet been explored with regard to children with RTT. OBJECTIVE: Assessing functional abilities of individuals with RTT due to CE intervention. DESIGN: A single subject, AB design. method: This study assessed the functional skills of three girls with RTT aged 3-5 years before and during participation in a CE programme. RESULTS: Gross motor function improvements were observed at the end of the intervention period. Gross motor skills declined slightly in all participants over the summer holidays but improved again a few months after recommencement of the educational year. CONCLUSION: Replication of this study with more subjects is justified as is comparison with other educational methods. A home intervention programme should be constructed to prevent decline of skills over the summer vacation.
Identifier
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<a href="http://doi.org/10.3109/17518423.2011.629374" target="_blank" rel="noreferrer noopener">10.3109/17518423.2011.629374</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2012
daily training program
Developmental Neurorehabilitation
Downs J
Lotan M
physical intervention
Rett syndrome
Schenker R
tone and motor problems
treadmill
Wine J
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1212/WNL.0b013e3182749e67" target="_blank" rel="noreferrer noopener">http://doi.org/10.1212/WNL.0b013e3182749e67</a>
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Title
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Video game-based coordinative training improves ataxia in children with degenerative ataxia
Publisher
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Neurology
Date
A point or period of time associated with an event in the lifecycle of the resource
2012
Subject
The topic of the resource
tone and motor problems; Friedreich's ataxia; physical intervention; video game-based coordinative training; ataxia; balance
Creator
An entity primarily responsible for making the resource
Ilg W; Schatton C; Schicks J; Giese M A; Schols L; Synofzik M
Description
An account of the resource
Objective: Degenerative ataxias in children present a rare condition where effective treatments are lacking. Intensive coordinative training based on physiotherapeutic exercises improves degenerative ataxia in adults, but such exercises have drawbacks for children, often including a lack of motivation for high-frequent physiotherapy. Recently developed whole-body controlled video game technology might present a novel treatment strategy for highly interactive and motivational coordinative training for children with degenerative ataxias. Methods: We examined the effectiveness of an 8-week coordinative training for 10 children with progressive spinocerebellar ataxia. Training was based on 3 Microsoft Xbox Kinect video games particularly suitable to exercise whole-body coordination and dynamic balance. Training was started with a laboratory-based 2-week training phase and followed by 6 weeks training in children's home environment. Rater-blinded assessments were performed 2 weeks before laboratorybased training, immediately prior to and after the laboratory-based training period, as well as after home training. These assessments allowed for an intraindividual control design, where performance changes with and without training were compared. Results: Ataxia symptoms were significantly reduced (decrease in Scale for the Assessment and Rating of Ataxia score, p = 0.0078) and balance capacities improved (dynamic gait index, p = 0.04) after intervention. Quantitative movement analysis revealed improvements in gait (lateral sway: p = 0.01; step length variability: p = 0.01) and in goal-directed leg placement (p 5 0.03). Conclusions: Despite progressive cerebellar degeneration, children are able to improvemotor performance by intensive coordination training. Directed training of whole-body controlled video games might present a highly motivational, cost-efficient, and home-based rehabilitation strategy to train dynamic balance and interaction with dynamic environments in a large variety of youngonset neurologic conditions. Classification of evidence: This study provides Class III evidence that directed training with Xbox Kinect video games can improve several signs of ataxia in adolescents with progressive ataxia as measured by SARA score, Dynamic Gait Index, and Activity-specific Balance Confidence Scale at 8 weeks of training. © 2012 American Academy of Neurology.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1212/WNL.0b013e3182749e67" target="_blank" rel="noreferrer noopener">10.1212/WNL.0b013e3182749e67</a>
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2012
ataxia
balance
Friedreich's ataxia
Giese M A
Ilg W
Neurology
physical intervention
Schatton C
Schicks J
Schols L
Synofzik M
tone and motor problems
video game-based coordinative training
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/" target="_blank" rel="noreferrer noopener">http://doi.org/</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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The effect of hand splints on stereotypic hand behavior in Rett's syndrome
Publisher
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Turkish Journal of Pediatrics
Date
A point or period of time associated with an event in the lifecycle of the resource
2002
Subject
The topic of the resource
tone and motor problems; Rett syndrome; physical intervention; hand splints; elbow restraint; stereotypic behavior
Creator
An entity primarily responsible for making the resource
Bumin G; Uyanik M; Kayihan H; Topcu M; Duger T
Description
An account of the resource
The purpose of this study was to examine the effect of hand splints and one elbow restraint on persistent stereotypic hand movements of four girls with Rett's syndrome. Among the most characteristic features of Rett's syndrome are stereotypic hand wringing and loss of previously acquired functional hand skills. Hand splints and one elbow restraint were used in this study. The subject's stereotypic hand behavior and functional hand use were calculated from five-minute segmental video tape recordings. The study consisted of three phases: baseline intervention, and withdrawal. All subjects demonstrated a decrease in stereotypic hand behavior after the application of hand splints. Although splints showed a positive effect on hand movements in Rett's syndrome, they could also lead to other, undesirable, movements, Whether splints have a positive effect on the functional use of the hand should be investigated in more subjects.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/" target="_blank" rel="noreferrer noopener"></a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2002
Bumin G
Duger T
elbow restraint
hand splints
Kayihan H
physical intervention
Rett syndrome
stereotypic behavior
tone and motor problems
Topcu M
Turkish Journal of Pediatrics
Uyanik M
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/s0387-7604(12)80202-6" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/s0387-7604(12)80202-6</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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The use and effectiveness of elbow splints in the Rett syndrome
Publisher
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Brain and Development
Date
A point or period of time associated with an event in the lifecycle of the resource
1990
Subject
The topic of the resource
tone and motor problems; Rett syndrome; physical intervention; elbow splints; stereotypic hand behavior; stereotypy; occupational therapy
Creator
An entity primarily responsible for making the resource
Aron M
Description
An account of the resource
Incessant hand to mouth movements are often noted as part of the movement disorder of the hands in the Rett syndrome (RS). Elbow splints were designed to inhibit this behavior and prevent further injury to the hands. A study of eight RS patients was conducted to determine the effectiveness of splinting. Results were very positive and indicated increased socialization, increased interaction with the environment, decreased hand to mouth movements, and decreased hand wringing behavior.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1016/s0387-7604(12)80202-6" target="_blank" rel="noreferrer noopener">10.1016/s0387-7604(12)80202-6</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
1990
Aron M
Brain and Development
elbow splints
Occupational Therapy
physical intervention
Rett syndrome
stereotypic hand behavior
stereotypy
tone and motor problems