1
40
2
-
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
Citation List Month
Backlog
URL Address
<a href="http://doi.org/10.1002/ppul.20725" target="_blank" rel="noreferrer">http://doi.org/10.1002/ppul.20725</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Lung disease in Niemann-Pick disease
Publisher
An entity responsible for making the resource available
Pediatric Pulmonology
Date
A point or period of time associated with an event in the lifecycle of the resource
2007
Subject
The topic of the resource
Child; Female; Humans; Male; Prognosis; Severity of Illness Index; Biopsy; Preschool; infant; Q3 Literature Search; Diagnosis; Differential; Lung Diseases; Respiratory Function Tests; Bronchoalveolar Lavage; Bronchoalveolar Lavage Fluid/cytology; Interstitial/diagnosis/etiology/physiopathology; Niemann-Pick Diseases/complications; Radiography; Thoracic
Creator
An entity primarily responsible for making the resource
Guillemot N; Troadec C; de Villemeur TB; Clement A; Fauroux B
Description
An account of the resource
BACKGROUND: Lung involvement in children with Niemann-Pick disease has rarely been studied systematically. OBJECTIVE: To assess the involvement of the lung and the value of bronchoalveolar lavage in children with Niemann-Pick diseases. DESIGN: Retrospective analysis of patient records. PATIENTS: Thirteen patients, with type A (n = 1), type B (n = 10), and type C (n = 2) Niemann-Pick disease, aged 2 months to 9 years at diagnosis, were included in the study. INTERVENTIONS: Lung involvement was assessed by clinical evaluation, chest radiograph, lung computed tomography (CT) scan, pulmonary function tests, and bronchoalveolar lavage fluid analysis. RESULTS: Respiratory symptoms were present at diagnosis in 10 patients and developed during follow up in the three other patients. All patients showed signs of interstitial lung disease on chest X-ray and lung CT scan. Bronchoalveolar lavage fluid analysis (n = 7) revealed a marked accumulation of foamy macrophages (Niemann-Pick cells) in all patients. At follow up, one patient died of respiratory failure, five patients required long term oxygen therapy and seven other patients presented a chronic obstructive pulmonary disease (n = 6) or chronic cough (n = 1). CONCLUSION: Lung disease was observed in all the patients included in the present study. Bronchoalveolar lavage may be useful in Niemann-Pick diseases by showing the presence of characteristic Niemann-Pick cells.
2007
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1002/ppul.20725" target="_blank" rel="noreferrer">10.1002/ppul.20725</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
Type
The nature or genre of the resource
Journal Article
2007
Backlog
Biopsy
Bronchoalveolar Lavage
Bronchoalveolar Lavage Fluid/cytology
Child
Clement A
de Villemeur TB
Diagnosis
Differential
Fauroux B
Female
Guillemot N
Humans
Infant
Interstitial/diagnosis/etiology/physiopathology
Journal Article
Lung Diseases
Male
Niemann-Pick Diseases/complications
Pediatric Pulmonology
Preschool
Prognosis
Q3 Scoping Review Results
Radiography
Respiratory Function Tests
Severity Of Illness Index
Thoracic
Troadec C
-
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
Citation List Month
Backlog
URL Address
<a href="http://doi.org/10.1503/cmaj.080072" target="_blank" rel="noreferrer">http://doi.org/10.1503/cmaj.080072</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Management of acute asthma in adults in the emergency department: nonventilatory management
Publisher
An entity responsible for making the resource available
Canadian Medical Association Journal
Date
A point or period of time associated with an event in the lifecycle of the resource
2010
Subject
The topic of the resource
Female; Humans; Pregnancy; Adult; Risk Factors; Acute Disease; Oxygen Inhalation Therapy; Patient Admission; Emergency Service; decision making; Radiography; Thoracic; Hospital; Blood Gas Analysis; Oxygen/blood; Airway Obstruction/diagnosis; Forced Expiratory Volume; Recurrence/prevention & control; Adrenal Cortex Hormones/therapeutic use; Asthma/diagnosis/therapy; Bronchodilator Agents/therapeutic use; Magnesium Sulfate/therapeutic use; Oximetry; Peak Expiratory Flow Rate
Creator
An entity primarily responsible for making the resource
Hodder R; Lougheed MD; Rowe BH; FitzGerald JM; Kaplan AG; McIvor RA
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1503/cmaj.080072" target="_blank" rel="noreferrer">10.1503/cmaj.080072</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
Type
The nature or genre of the resource
Journal Article
Description
An account of the resource
2010
2010
Acute Disease
Adrenal Cortex Hormones/therapeutic use
Adult
Airway Obstruction/diagnosis
Asthma/diagnosis/therapy
Backlog
Blood Gas Analysis
Bronchodilator Agents/therapeutic use
Canadian Medical Association Journal
Decision Making
Emergency Service
Female
FitzGerald JM
Forced Expiratory Volume
Hodder R
Hospital
Humans
Journal Article
Kaplan AG
Lougheed MD
Magnesium Sulfate/therapeutic use
McIvor RA
Oximetry
Oxygen Inhalation Therapy
Oxygen/blood
Patient Admission
Peak Expiratory Flow Rate
Pregnancy
Radiography
Recurrence/prevention & control
Risk Factors
Rowe BH
Thoracic