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Text
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URL Address
<a href="http://doi.org/10.1136/adc.73.1.77" target="_blank" rel="noreferrer">http://doi.org/10.1136/adc.73.1.77</a>
Dublin Core
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Title
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Behaviour in mucopolysaccharide disorders
Publisher
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Archives Of Disease In Childhood
Date
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1995
Subject
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Child; Female; Humans; Male; Prevalence; Data Collection; Parents; Family Health; Self-Help Groups; Preschool; Q3 Literature Search; Mucopolysaccharidoses/complications; Mucopolysaccharidosis III/psychology; Aggression; Child Behavior Disorders/complications; Mucopolysaccharidosis II/psychology; Sleep Disorders/complications
Creator
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Bax MC; Colville GA
Description
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This paper reports a study of the nature and prevalence of behaviour problems in 258 children with mucopolysaccharide disorders. Questionnaire data obtained through the post was supplemented by home visits to 42 families in the sample and by regular discussions with families at meetings of the Society for Mucopolysaccharide Diseases. High rates of behaviour problems were found, particularly in children with Sanfilippo's and Hunter's disease aged 5 to 9 years. These included destructiveness, restlessness, and aggressiveness. Sleep problems were common across subtypes with an overall prevalence of 66%. Parents reported that they received little or no support in the management of these difficult behaviours. It is concluded that behaviour problems are a primary feature of the mucopolysaccharide disorders and place a major strain on families. Services to help families cope with these problems are urgently needed.
1995
Identifier
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<a href="http://doi.org/10.1136/adc.73.1.77" target="_blank" rel="noreferrer">10.1136/adc.73.1.77</a>
Rights
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Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
Type
The nature or genre of the resource
Journal Article
1995
Aggression
Archives of Disease in Childhood
Backlog
Bax MC
Child
Child Behavior Disorders/complications
Colville GA
Data Collection
Family Health
Female
Humans
Journal Article
Male
Mucopolysaccharidoses/complications
Mucopolysaccharidosis II/psychology
Mucopolysaccharidosis III/psychology
Parents
Preschool
Prevalence
Q3 Scoping Review Results
Self-Help Groups
Sleep Disorders/complications