1
40
2
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
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URL Address
<a href="http://doi.org/10.1016/j.nmd.2014.01.003" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.nmd.2014.01.003</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
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Hammersmith Functional Motor Scale and Motor Function Measure-20 in non ambulant SMA patients
Publisher
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Neuromuscular Disorders
Date
A point or period of time associated with an event in the lifecycle of the resource
2014
Subject
The topic of the resource
responsiveness; Neurosciences & Neurology; Spinal muscular atrophy; trial; spinal muscular-atrophy; validation; neuromuscular diseases; Outcome measures; walk test; tone and motor problems; SMA1; tool development; scale development; HMFS; MFM
Creator
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Mazzone E; De Sanctis R; Fanelli L; Bianco F; Main M; van den Hauwe M; Ash M; de Vries R; Mata J F; Schaefer K; D'Amico A; Colia G; Palermo C; Scoto M; Mayhew A; Eagle M; Servais L; Vigo M; Febrer A; Korinthenberg R; Jeukens M; de Viesser M; Totoescu A; Voit T; Bushby K; Muntoni F; Goemans N; Bertini E; Pane M; Mercuri E
Description
An account of the resource
The aim of this prospective longitudinal multi centric study was to evaluate the correlation between the Hammersmith Functional Motor Scale and the 20 item version of the Motor Function Measure in non ambulant SMA children and adults at baseline and over a 12 month period. Seventy-four non-ambulant patients performed both measures at baseline and 49 also had an assessment 12 month later. At baseline the scores ranged between 0 and 40 on the Hammersmith Motor function Scale and between 3 and 45 on the Motor Function Measure 20. The correlation between the two scales was 0.733. The 12 month changes ranged between 11 and 4 for the Hammersmith and between 11 and 7 for the Motor Function Measure 20. The correlation between changes was 0.48. Our results suggest that both scales provide useful information although they appeared to work differently at the two extremes of the spectrum of abilities. The Hammersmith Motor Function Scale appeared to be more suitable in strong non ambulant patients, while the Motor Function Measures appeared to be more sensitive to capture activities and possible changes in the very weak patients, including more items capturing axial and upper limb activities. The choice of these measures in clinical trials should therefore depend on inclusion criteria and magnitude of expected changes. (C) 2014 Published by Elsevier B.V.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1016/j.nmd.2014.01.003" target="_blank" rel="noreferrer noopener">10.1016/j.nmd.2014.01.003</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2014
Ash M
Bertini E
Bianco F
Bushby K
Colia G
D'Amico A
De Sanctis R
de Viesser M
de Vries R
Eagle M
Fanelli L
Febrer A
Goemans N
HMFS
Jeukens M
Korinthenberg R
Main M
Mata J F
Mayhew A
Mazzone E
Mercuri E
MFM
Muntoni F
Neuromuscular Diseases
Neuromuscular Disorders
Neurosciences & Neurology
Outcome measures
Palermo C
Pane M
responsiveness
scale development
Schaefer K
Scoto M
Servais L
SMA1
Spinal Muscular Atrophy
spinal muscular-atrophy
tone and motor problems
tool development
Totoescu A
trial
VALIDATION
van den Hauwe M
Vigo M
Voit T
walk test
-
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1016/j.nmd.2009.11.014" target="_blank" rel="noreferrer noopener">http://doi.org/10.1016/j.nmd.2009.11.014</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
The Children's Hospital of Philadelphia Infant Test of Neuromuscular Disorders (CHOP INTEND): Test development and reliability
Publisher
An entity responsible for making the resource available
Neuromuscular Disorders
Date
A point or period of time associated with an event in the lifecycle of the resource
2010
Subject
The topic of the resource
tone and motor problems; SMA1; tool development; scale development; CHOP INTEND
Creator
An entity primarily responsible for making the resource
Glanzman A M; Mazzone E; Main M; Pelliccioni M; Wood J; Swoboda K J; Scott C; Pane M; Messina S; Bertini E; Mercuri E; Finkel R S
Description
An account of the resource
The motor skills of patients with spinal muscular atrophy, type I (SMA-I) are very limited. It is difficult to quantify the motor abilities of these patients and as a result there is currently no validated measure of motor function that can be utilized as an outcome measure in clinical trials of SMA-I. We have developed the Children's Hospital of Philadelphia Infant Test of Neuromuscular Disorders (" CHOP INTEND" ) to evaluate the motor skills of patients with SMA-I. The test was developed following the evaluation of 26 infants with SMA-I mean age 11.5. months (1.4-37.9. months) with the Test of Infant Motor Performance and The Children's Hospital of Philadelphia Test of Strength in SMA, a newly devised motor assessment for SMA. Items for the CHOP INTEND were selected by an expert panel based on item mean and standard deviation, item frequency distribution, and Chronbach's alpha. Intra-rater reliability of the resulting test was established by test-retest of 9 infants with SMA-I over a 2. month period; Intraclass correlation coefficient (ICC) (3,1) = 0.96. Interrater reliability was by video analysis of a mixed group of infants with neuromuscular disease by 4 evaluators; ICC (3,4) = 0.98 and in a group of 8 typically developing infants by 5 evaluators ICC (3,5) = 0.93. The face validity of the CHOP INTEND is supported by the use of an expert panel in item selection; however, further validation is needed. The CHOP INTEND is a reliable measure of motor skills in patients with SMA-I and neuromuscular disorders presenting in infancy. © 2009 Elsevier B.V.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1016/j.nmd.2009.11.014" target="_blank" rel="noreferrer noopener">10.1016/j.nmd.2009.11.014</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
2010
Bertini E
CHOP INTEND
Finkel R S
Glanzman A M
Main M
Mazzone E
Mercuri E
Messina S
Neuromuscular Disorders
Pane M
Pelliccioni M
scale development
Scott C
SMA1
Swoboda K J
tone and motor problems
tool development
Wood J