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Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Treatment of Symptoms in Children with Q3 Conditions Scoping Review Results
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
URL Address
<a href="http://doi.org/10.1111/j.1525-1470.1997.tb00991.x" target="_blank" rel="noreferrer noopener">http://doi.org/10.1111/j.1525-1470.1997.tb00991.x</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Constipation in epidermolysis bullosa: successful treatment with a liquid fiber-containing formula
Publisher
An entity responsible for making the resource available
Pediatric Dermatology
Date
A point or period of time associated with an event in the lifecycle of the resource
1997
Subject
The topic of the resource
Adolescent Child; Child; Formulated; Humans; Male; Preschool; Constipation/co [Complications]; Constipation/th [Therapy]; Epidermolysis Bullosa/co [Complications]; Female; Food; constipation; Epidermolysis Bullosa; pharmacologic intervention; fiber-containing liquid formula Enrich
Creator
An entity primarily responsible for making the resource
Haynes L; Atherton D; Clayden G
Description
An account of the resource
In epidermolysis bullosa (EB), chronic constipation, painful defecation, and fecal impaction frequently contribute to malnutrition and growth failure. Standard treatments for constipation, such as increased intake of conventional dietary fiber and fluids and/or the use of laxatives and stool softeners, are largely unsuccessful. We evaluated by questionnaire the use of a fiber-containing liquid formula (Enrich) in 20 chronically constipated children with dystrophic EB. All derived substantial improvement in constipation when taking 250 to 750 ml Enrich per day. We recommend that such a fiber-containing food be prescribed for chronic constipation in EB. In cases of fecal impaction, this should be preceded by bowel cleansing.
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1111/j.1525-1470.1997.tb00991.x" target="_blank" rel="noreferrer noopener">10.1111/j.1525-1470.1997.tb00991.x</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
1997
Adolescent Child
Atherton D
Child
Clayden G
Constipation
Constipation/co [Complications]
Constipation/th [Therapy]
epidermolysis bullosa
Epidermolysis Bullosa/co [Complications]
Female
fiber-containing liquid formula Enrich
Food
Formulated
Haynes L
Humans
Male
Pediatric Dermatology
pharmacologic intervention
Preschool
-
Text
A resource consisting primarily of words for reading. Examples include books, letters, dissertations, poems, newspapers, articles, archives of mailing lists. Note that facsimiles or images of texts are still of the genre Text.
Citation List Month
Backlog
URL Address
<a href="http://doi.org/10.1212/01.WNL.0000167428.12417.B2" target="_blank" rel="noreferrer">http://doi.org/10.1212/01.WNL.0000167428.12417.B2</a>
Dublin Core
The Dublin Core metadata element set is common to all Omeka records, including items, files, and collections. For more information see, http://dublincore.org/documents/dces/.
Title
A name given to the resource
Late-onset neurologic disease in glutaryl-CoA dehydrogenase deficiency
Publisher
An entity responsible for making the resource available
Neurology
Date
A point or period of time associated with an event in the lifecycle of the resource
2005
Subject
The topic of the resource
Humans; Male; Aged; Treatment Outcome; Disease Progression; Magnetic Resonance Imaging; Food; Q3 Literature Search; Brain Diseases; Age of Onset; DNA Mutational Analysis; Mutation/genetics; Metabolic; Atrophy/enzymology/genetics/physiopathology; Carnitine/therapeutic use; Cerebral Cortex/enzymology/pathology/physiopathology; Cognition Disorders/enzymology/genetics/physiopathology; Formulated; Glutaryl-CoA Dehydrogenase/deficiency; Inborn/enzymology/genetics/physiopathology; Lateral Ventricles/pathology; Movement Disorders/enzymology/genetics/physiopathology; Myelinated/pathology; Nerve Fibers
Creator
An entity primarily responsible for making the resource
Kulkens S; Harting I; Sauer S; Zschocke J; Hoffmann GF; Gruber S; Bodamer OA; Kolker S
Description
An account of the resource
Neurologic disease in glutaryl-CoA dehydrogenase (GCDH) deficiency usually presents with acute encephalopathic crises before 2 years of age. The authors report two previously asymptomatic patients with macrocephaly presenting with progressive neurologic deterioration and a severe leukoencephalopathy during adolescence or adulthood.
2005
Identifier
An unambiguous reference to the resource within a given context
<a href="http://doi.org/10.1212/01.WNL.0000167428.12417.B2" target="_blank" rel="noreferrer">10.1212/01.WNL.0000167428.12417.B2</a>
Rights
Information about rights held in and over the resource
Article information provided for research and reference use only. PedPalASCNET does not hold any rights over the resource listed here. All rights are retained by the journal listed under publisher and/or the creator(s).
Type
The nature or genre of the resource
Journal Article
2005
Age of Onset
Aged
Atrophy/enzymology/genetics/physiopathology
Backlog
Bodamer OA
Brain Diseases
Carnitine/therapeutic use
Cerebral Cortex/enzymology/pathology/physiopathology
Cognition Disorders/enzymology/genetics/physiopathology
Disease Progression
DNA Mutational Analysis
Food
Formulated
Glutaryl-CoA Dehydrogenase/deficiency
Gruber S
Harting I
Hoffmann GF
Humans
Inborn/enzymology/genetics/physiopathology
Journal Article
Kolker S
Kulkens S
Lateral Ventricles/pathology
Magnetic Resonance Imaging
Male
Metabolic
Movement Disorders/enzymology/genetics/physiopathology
Mutation/genetics
Myelinated/pathology
Nerve Fibers
Neurology
Q3 Scoping Review Results
Sauer S
Treatment Outcome
Zschocke J